External auditory canal cholesteatoma is very rare disease in otology. External auditory canal cholesteatoma and keratosis obturans have previously been considered to represent the same disease process. Recently Piepergerdes et al. considered these to be two different clinical and pathologic process. External auditory canal cholesteatoma presents as otorrhea with chronic, dull pain secondary to an invasion of squamous tissue into a localized area of periosteitis in the canal wall. Keratosis obturans presents as conductive hearing loss and usually acute, severe pain secondary to the accumulation of large plugs of desquamated keratin in the ear canal. Recently, authors have experienced one case of extensive left external auditory canal cholesteatoma in 55 years old female who had surgical correction with good operation result.