The Vogt-Koyanagi-Harada Syndrome is a relatively rare multi-system disease including eye, central nervous system, ear, and skin. This syndrome has been frequently reported by ophthalmologist or neurologist, since the predominating signs and symptoms fall in the realm of these two specialities. Therefore, there has been a noticeable absence in otolaryngologic literature and the information regarding the type of sensorineural hearing loss has not been well evaluated and the temporal bone pathology has not yet been demonstrated. In this report we will report two cases focusing on otologic aspect, and hope that more of these patients will be evaluated otologically in the future.